HLH. 아주 흔하지 않은데 그래도 발병하기에 DDx에는 끼어넣어야하는 질환. Introduction and epidemiology Hemophagocytic lymphohistiocytosis (HLH) is a disease with major diagnostic and therapeutic difficulties. HLH comprises two different conditions that may be difficult to distinguish from one another: a primary and a secondary form1)Primary HLH-The primary autosomal recessive form, familial hemophagocytic lymphohistiocytos..
